A Case of Swyer-James Syndrome, with Reference to Pathophysiologic and Etiologic Aspect

SHIMAMOTO Yoriko

SHIMAMOTO Hiroyuki

MATSUURA Yuichiro

TAMURA Mutuo

YAMASHINA Hideki

HIGO Masanori

FUJII Takanori

KINOSHITA Hirufumi

KIMURA Shojiro

HIRAO Koichi

TAKEDA Hiroyuki

Hiroshima Journal of Medical Sciences

[PISSN] 0018-2052

[EISSN] 2433-7668

[NCID] AA00664312

A 21-year-old male of Swyer-James syndrome is presented with clinical, angiographic, bronchographic and scintigraphic studies. He had a past history of recurrent bronchial asthma. A chest roentgenogram revealed unilateral hyperlucency of the left lung without any changes in volume. The small size of the pulmonary artery and its branches of the left lower lobe was visible by pulmonary angiography. Bronchography showed the bronchiectatic changes which consisted of moderate bronchial dilatation in an irregular beaded pattern with clubbed or tapered ends accompanied by absence of alveolar filling. A perfusion lung scan using 99mTc-macroaggregated albumin (99mTc-MAA) illustrated a perfusion defect in the left lower lobe. It was thought that recurrent pulmonary infections and asthmatic attacks were responsible for a pathological condition of this disease.

Swyer-James syndrome

Unilateral hyperlucency

Bronchiectasis

Narrowing pulmonary artery

Medical sciences [ 490 ]

eng

Hiroshima University School of Medicine

[ISSN] 0018-2052

[NCID] AA00664312

[PMID] 3771274