Pulmonary Lymphangiomyomatosis in Childhood? : Marked Smooth Muscle Cell Proliferation of the Lung in a Preadolescent Girl with Repeated Pneumothorax and Progressive Dyspnea

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Title ( eng )
Pulmonary Lymphangiomyomatosis in Childhood? : Marked Smooth Muscle Cell Proliferation of the Lung in a Preadolescent Girl with Repeated Pneumothorax and Progressive Dyspnea
Creator
Sakano Takashi
Hamasaki Takashi
Kawaguchi Yoshinori
Tanaka Yoshito
Ueda Kazuhiro
Hiramoto Takehiko
Source Title
Hiroshima Journal of Medical Sciences
Volume 38
Issue 3
Start Page 147
End Page 149
Journal Identifire
[PISSN] 0018-2052
[EISSN] 2433-7668
[NCID] AA00664312
Abstract
A 13-year-old girl with repeated spontaneous pneumothorax and progressive dyspnea is described. The biopsy specimen of the lung showed marked proliferation of smooth muscle cells in the thickened bullous wall and alveolar septa, which was similar to the findings of the pulmonary lymphangiomyomatosis. Pulmonary lymphangiomyomatosis is one of the diseases which should be considered when children have progressive dyspnea, chylous effusions and repeated spontaneous pneumothorax.
Keywords
Pulmonaiy lymphangiomyomatosis
Smooth muscle cell proliferation
NDC
Medical sciences [ 490 ]
Language
eng
Resource Type departmental bulletin paper
Publisher
Hiroshima University Medical Press
Date of Issued 1989-09
Publish Type Version of Record
Access Rights open access
Source Identifier
[ISSN] 0018-2052
[NCID] AA00664312
[PMID] 2584060