A 1-year-and-1-month-old female patient diagnosed with achondroplasia (ACH), underwent foramen magnum decompression under general anesthesia. Difficult airway management was predicted at the induction of general anesthesia, and Airway ScopeTM was successfully used in tracheal intubation. Heat retention was observed during the anesthetic management, supposedly due to the congenital shortness of her four limbs. General anesthesia, including airway management and strict control of body temperature, should be carefully planned in pediatric patients with ACH.