A subclavian artery aneurysm associated with Neurofibromatosis type 1 (NF 1) is extremely rare. We report a ruptured pseudo-aneurysm of the subclavian artery in a patient with NF 1 treated with endovascular surgery. A 51 year old man with NF 1 presented with initially sudden left neck pain and continuous dysphagia. Radiological examination showed a pseudo-aneurysm of the left subclavian artery. Endovascular stenting and coil embolisation was performed to prevent rebleeding and the lesion was completely obliterated. Follow-up angiography at 3 months revealed good flow through the stent without flow into the pseudo-aneurysm. Our patient is the first reported example of successful endovascular treatment for a ruptured subclavian artery pseudo-aneurysm associated with NF 1. Endovascular stenting and coil embolisation for the ruptured subclavian artery pseudo-aneurysm was very effective.